A 59-year-old man was admitted to the hospital because of melena and dizziness. Barium X-ray study of the small intestine revealed a filling defect in the ileum. Partial resection of the ileum was performed with a diagnosis of ileal tumor. The tumor was 1.8×1.5×1.8cm in size, and located on a site, 60cm oral to the Bauhin's valve.
Histopathological diagnosis was leiomyoblastoma. Thereafter the patient had liver metastasis and peritoneal dissemination which were resected respectively, however, he died of metastases to the whole body 4 years and 2 months after the initial operation. Leiomyoblastoma of the small intestine is relatively rare and presents difficulty in diagnosis of the degree of malignancy of the tumor. Surgical resection of the tumor is said to carry a good prognosis. Nevertheless, some patients have a poor prognosis like this case and careful observation of clinical course would be mandatary.