A 54-year-old man was referred to our emergency room due to upper abdominal pain. Computed tomography revealed celiac artery dissection, the dissecting aneurysm of the splenic artery and bloody ascites. The patient was diagnosed with rupture of the dissecting aneurysm of the splenic artery due to isolated spontaneous celiac artery dissection (ISCAD). He underwent laparotomy and ligation of the splenic artery emergently. We report a rare case of ISCAD with rupture of the dissecting aneurysm of the splenic artery.