A case of Di George Syndrome is presented.
The results of the clinical oral findings are as follows
1) The patient was a 3-year and 11-month old boy.
2) The general examination showed delayed growth for one year.
3) Roentgenographic examination showed a regional enamel hypoplasia in all primary teeth, but radiographic findings showed no anomaies.
4) It seems that enamel hypoplasia was caused by the decrease of serum Ca concentration in a hypoparathyroidism.
5) Enamel hypoplasia was ameliorated by the improvement of the whole body condition.