Rett syndrome patients are found only in girls and show symptoms such as autism, mental retardation and cerebral palsy. The disorder is also characterized by the stereotypic hand activities, and disability in walking and pronounciation. Little is known about the specific characteristics of the dental traits in Rett syndrome children owing to the lack of case reports. The findings of 14-year-old girl affected with the Rett syndrome, who had undergone the dental treatment under the general anesthesia at Kyushu University Dental Hospital, were as follows.
1. Lower body height and weight were found.
2. Osteoarthritis of the spine was observed.
3. Bone age was advanced by 1-2 years older than the chronological age.
4. The mesio-distal diameters of the tooth crowns were smaller than the mean values.
5. Lateral cephalometric analysis showed micrognathism.
6. Labial inclinations of the upper and lower anterior teeth were found with tongue thrusting.
7. The patient received the dental treatment under the general anesthesia, due to severe mental retardation and definitive uncooperation.