The patient was a 59-year-old woman on maintenance hemodialysis for unknown chronic renal failure from 2010. She recognized worsening skin itching from the beginning of 2014, and extensive exudative erythema appeared on the trunk and limbs and blisters on the palm and inside of the thigh in May. Therefore, she was to be admitted to our hospital at the beginning of June, but just before that, a fistula occluded. Thus, she was treated at another hospital and then transferred to our hospital. She started treatment with oral prednisolone (PSL) with a diagnosis of bullous pemphigoid from a skin biopsy and a high level of anti-BP180 antibodies. At first, she continued hemodialysis using a catheter, but it was removed because of catheter infection. With the improvement of her skin condition, she continued hemodialysis using a fistula from the fifth hemodialysis after being transferred. The patient was discharged at the end of June. There have been few reports of bullous pemphigoid in maintenance hemodialysis patients, so we report this case along with a review of relevant literature.