Case 1 : A 41-year-old woman presented with abdominal pain. MRI scan of the abdomen revealed a soft tissue mass in the pelvic cavity and abdominoperineal resection for the tumor was performed. The histopathological diagnosis was aggressive angiomyxoma (AAM). Case 2 : A 36-year-old woman patient presented to the Department of Gynecology in our hospital because of uterine bleeding. MRI scan revealed a myoma of the uterus and a soft tissue mass in the pelvic cavity. We performed enucleatic myomectomy + tumorectomy. The histopathological diagnosis was AAM. Case 3 : A 64-year-old woman patient presented with a tumor protruding from the anus at defecation. Based on CT findings, it was diagnosed as a condition where a pelvic soft tissue tumor had directly invaded the rectum and exposed from the anus. We performed tumorectomy + partial resection of the rectum. The histopathological diagnosis was AAM.

AAM is a rare mesenchymal tumor which often affects the genital organs, perineum, and pelvis in women of reproductive age. Our experiences with three cases of AAM are presented here, together with a review of the literature.