A 55-year-old woman was referred to our hospital because of an abnormal chest X-ray shadow in the right upper lung field. A chest wall mass was observed just below the first right costal cartilage in CT. Neurogenic tumor was suspected. We performed thoracoscopic surgery for this. The tumor was parietal extrapleural mass protruding from the first intercostal space. We excised this tumor with the parietal pleura. The pathological diagnosis was desmoid tumor. Local recurrence occurred one year after the operation. The tumor was present in the dorsal side of the right first rib, and had destroyed a part of the rib. We performed re-operation for this. The tumor was resected en bloc together with the right brachiocephalic vein side wall, part of the 1&2 ribs and right lung upper lobe. We rebuilt the defect of the chest wall by using Composix mesh. The pathological diagnosis was desmoid tumor too. She was discharged on the 13th postoperative day. We gave continuous administration of meloxicam followed by radiotherapy at 54Gy in our clinic. There has been no recognizable re-recurrence as of 2 years and 7 months after the second surgery. We have experienced a surgical case of a locally recurred chest wall desmoid tumor.