A low-grade fibromyxoid sarcoma (LGFMS) is a rare soft tissue tumor, originally described by Evans in 1987.
We experienced a 73-year-old male who presented with a mass in his left deep neck. As a treatment, the mass was surgically removed and it was diagnosed as a low-grade fibromyxoid sarcoma (LGFMS), a very rare tumor.
LGFMS is not only a rare sarcoma, but also shows a high rate of local recurrence and distant metastasis.
Additional radiotherapy was performed because of a positive surgical margin. The postoperative course of the patient has been uneventful without any recurrence or metastasis.